X-Message-Number: 28724 Date: Wed, 6 Dec 2006 11:57:15 -0800 (PST) From: Subject: fly longevity experiment wish list [If anybody is willing to donate a small sample of either memantine or rapamycin for a fly longevity test please contact me privately. Fly longevity is known to be limited by motor neuron degeneration, and these prescription items may affect this.] J Neural Transm Suppl. 2004;(68):117-22. The N-methyl-D-aspartate antagonist memantine retards progression of Huntington's disease. According to the excitotoxicity hypothesis, neurotoxicity due to glutamate is regarded as potential factor in the progredient neurodegeneration of Huntington's disease (HD). Memantine, as a glutamate receptor antagonist, should counteract this mechanism. Its effectiveness (up to 30 mg/day) with regard to retardation of progression was thus examined in 27 HD patients in a two year, open and multicentre trial. The results suggest that memantine treatment of HD may be useful in terms of retardation of the progression of the disorder. Mol Aspects Med. 2006 October - December;27(5-6):520-527. Epub 2006 Sep 14. Role of autophagy in the clearance of mutant huntingtin: A step towards therapy? Macroautophagy (henceforth referred to simply as autophagy) is a bulk degradation process involved in the clearance of long-lived proteins, protein complexes and organelles. A portion of the cytosol, with its contents to be degraded, is enclosed by double-membrane structures called autophagosomes/autophagic vacuoles, which ultimately fuse with lysosomes where their contents are degraded. In this review, we will describe how induction of autophagy is protective against toxic intracytosolic aggregate-prone proteins that cause a range of neurodegenerative diseases. Autophagy is a key clearance pathway involved in the removal of such proteins, including mutant huntingtin (that causes Huntington's disease), mutant ataxin-3 (that causes spinocerebellar ataxia type 3), forms of tau that cause tauopathies, and forms of alpha-synuclein that cause familial Parkinson's disease. Induction of autophagy enhances the clearance of both soluble and aggregated forms of such proteins, and protects against toxicity of a range of these mutations in cell and animal models. Interestingly, the aggregates formed by mutant huntingtin sequester and inactivate the mammalian target of rapamycin (mTOR), a key negative regulator of autophagy. This results in induction of autophagy in cells with these aggregates. Rate This Message: http://www.cryonet.org/cgi-bin/rate.cgi?msg=28724