X-Message-Number: 3277 Date: Sun, 16 Oct 1994 17:44:22 -0400 (EDT) From: Subject: SCI.CRYONICS COMPREHENSIVE REVIEW OF AGEING Date sent: 16-OCT-1994 17:41:22 >Newsgroups: bionet.molbio.ageing > > > >Contents include: > >1.) brief descriptions of topics generally encompassed, in order to > indicate what's going on in general; and >2.) a few references, reviews and/or recent publications regarding > topics in aging research. All references should of course be taken > to include "and references therein". > > >Thanks, > >-- Tim Hughes > > >I. Definition of Aging > > A. Senescence - Senescence refers to intrinsic adverse changes > during aging in an organism. Strictly this is > manifest as an increasing likelihood of death as >a function of time, measured either from birth or from >some developmental stage. [Also, strictly the term "senescence" > should be used instead of "aging" in this FAQ but I >haven't bothered.] Cell senescence refers > to the limited proliferative capacity of cultured >somatic cells (see below). > > 1. Gompertz Curve: A mathematical function called > the "Gompertz curve" can be derived to describe > expected mortality statistics for a population of10%organisms whose >probability of death increases as a function >of time.Many populations (including humans) > demonstrate a survival curve which >can be fit closely by a Gompertz curve. A > critical parameter in the Gompertz expression is >the MRDT (mortalitay rate doubling time) which is > considered the index of how fast organisms in > the population senesce, and it has been suggested > that in scientific studies true slowing of the > aging process occurs only when the MRDT increases, > regardless of other aging parameters (i.e., mean, > mode, maximum lifespan). > >General references on the study of aging: >Finch, C. E. 1991. Longevity, Senescence, and the > Genome. Univ. Chicago Press.843 pages including > references. > >Martin, George R. et al. 1993. Aging - Causes and 4 > > Defenses. Annu. Rev. Med. 44:419-29. A quick > overview, not entirely comprehensive but easy reading. > >Kirkwood, T.B.L. and Cremer, T. Cytogerontology Since > 1881: A Reappraisal of August Weismann and a Review > of Modern Progress. Human Genetics (1982) 60:101-121. > A historical review of aging theories and arguments. > > >II. Theories and evidence regarding the > aging of multicellular organisms > >A. General Arguments. >Population genetics [something I know little about] > argues that no genetic trait which is detrimental >late in life would be selected for, so >no genes can survive throughout a population whose >sole function is to cause senescence. The remaining >possibilites are as follows: >7 > >1. Antagonistic Plieotropy: It is possible for genes > which are benefical or necessary in youth or in >the short term to be detrimental in the long term. > An example is the cytochrome oxidase, a > metabolic enzyme [detoxifant, I think] which is > responsible for the initial step in transforming > a number of dietary compounds into mutagenic agents. >References: >Aeschbacher, H-U. and Turesky, R.J. (1991) > Mammalian cell mutagenicity and metabolism of > heterocyclic aromatic amines. Mutation > Research, 256:235-250. > >2. Longevity Assurance Genes: t is also possible > that genes which are designed to protect us > from detriment be finite in capacity, as no > selection may exist for alleles which protect > for longer than the lifetime. [Example: > genes involved in DNA damage control in somatic >tissues.]21 > > >B. Disposable Soma Theory: It has been suggested that >the optimal allocation of energy for an organism >which reproduces repeatedly is to invest no more >energy in somatic maintenance than is necessary >to ensure reproduction. [The originaldea, >I believe, referred primarily to DNA damage.] >[Also, this argument seems unlikely to me to apply to >humans. My understanding is that we >consume 40% of our resting energy on brain activity, >and about 30% of all ATP generated on maintaining >transmembrane potentials (from which many cellular processes >are driven, I'm not sure how much of that is converted into >work and how much is lost by diffusion) >and maintain a fairly warm body temperature. This >suggests to me that >energy conservation is not a significant selective >advantage for mammals and humans in particular.] > >5 > >C. Somatic Mutation Hypothesis. > DNA is inherently unstable and is susceptible to >numerous modification and damaging agents. As >genetic material it requires constant maintenance. >One of the original ideas about the aging process >is that the accumulation of somatic mutations throughout >the lifespan is responsible for dysfunction of cells >and consequently of organs and individuals. This >has fallen out of favor as a mechanism for aging since >DNA damage would be expected to be fairly random, and >aging is largely consistent over a population. > >2. free radicals: Reactive oxygen species are produced > by mitochondria in oxidative phosphorylation, the > biochemical pathy that allows us to utilize oxygen > in energy production [conversion, rather]. Free > radical species can also be produced by ionozing > radiation. Free radicals can modify/damage a wide >range of cellular molecules including DNA, lipids >and proteins (see below).9 > > >2. carcinogens and mutagens: > >3. cancer: > >4. mitochondrial DNA damage: Mitochondria contain a > small genome which due to its proximity to > oxidative phosphorylation activity is more > susceptible to oxidation than the nuclear DNA. > Human mtDNA is 16.6 kb and encodes > a small portion of the peptides involved in >oxidative phosphorylation and also the rRNAs and > tRNAs needed to translate these genes. It has >een observed that the mutation rate of mtDNA >is higher than that of the nuclear DNA, and also >that there is a decline in oxidative phosphorylation >activity in some tissues with age. Mitochondrial >genetics is complex due to interaction with >nuclear genes, predominant maternal inheritance, >d the possibility that not all mitochondria in33a cell need to be genetically identical.Nonetheless > a number of genetic diseases are linked to mtDNA, >and that mutations in nuclear genes > can adversely affect mtDNA and/or oxidative >phosphorylation. > It has been proposed that accumulated mtDNA damage >is a mechanism in aging, and that mitochondria with >genomic deletions would be enriched due to a replicative >advantage. [As with anyheory involving genomic >instability, one must reconcile the fact that >babies are inevitably born young. In this case >the question is: how do babies escape getting mom's >20-40 year old mitochondria?] > References: > Wallace, D.C. (1992) Mitochondrial Genetics: A > Paradigm for Aging and Degenerative Diseases? > Science 256:628-632 (May 1 1992). > >5. apoptosis: >6 > >D. Endocrine cascade > > > >E. Cell Senescence. >A number of types of human cells will undergo >less than about 100 divisions when cultured >(grown in a dish or flask), at which point the cells >adopt a distinctive appearance and will not >divide any further. As stimulus to divide in mammalian >tissues consists mainly of signaling factors >it has been argued that senescence is a >tissue culture artifact due to improper or inadequate >signaling or an adaptive tolerance to signals. >In large enough sample sizes, however, >an inverse correlation between number >of divisions obtained and age of donor is >observed, and there also exists a rough correlation between >species lifespan and number of divisions obtained. >Furthermore cells from individuals with Werner's9 > > syndrome (premature aging) have a reduced proliferative >capacity. It has been proposed that cell senescence >occurs in vivo and could be >responsible for loss of homeostasis in tissues > of the elderly. Cells which senesce in culture include >fibroblasts, lymphocytes, various epithelial cells, >and adrenocortical cells. Tumor cells do not >senesce in culture and it has also been proposed >that senescence acts as a tumor-contromechanism >by providing an additional hurdle for growth-errant >cells. It is important to note that no direct evidence >for cell senescence occuring in vivo has yet been >obtained. > References: > Warner, H.R. et al. (1992) Control of Cell > Proliferation in Senescent Cells. Journal > of Gerontology 47(6):B185-B189. > >1. DNA synthesis inhibition > In an expression screen for cDNAs (expressed44 > > genes) in senescent cells which could inhibit > DNA synthesis in "young" cells, the SDI-1 gene > was cloned and found to be significantly up-regulated > in senescent cells compered with their young > counterparts. The gene was also cloned by > two other groups simultaneously using completely > different methods, and is thought to be the > primary element responsible for p53-dependent > cell-cycle arrest. > References: > Hunter, Tony (1993) Braking the cycle (minireview). > Cell 75:839-841 (Dec 3 '93). > >2. complementation studies: > Cultured cells can be fused to one another and > genetic properties analyzed in a manner analagous > to yeast mating. Early cell fusion experiments >clearly illustrated that senescence was a dominant > trait in fused cultured cells (i.e. fusions of young to >senescent are senescent; immortal to senescent are8 > >senescent.) This suggested that element(s) were >missing from immortal cells which could be provided >by senescent cells. To determine if immortal cells >were all lacking the same thing or had different >deletions, various immortal cells were fused, and >it was found that some complemented (rescued) >each other. In a specific case, a single inserted >chromosome was sufficient to restore senescence. >These complementation studies have recently been >challenged, with apparently different results >obtained using somewhat different methods. > References: > Pereira-Smith, O.M. & Smith, J.R. (1988) Genetic > analysis of indefinite division in human > cells: Identification of four complementation > groups. PNAS 85:6042-6046. > Ning, Y. et.al. (1991) Genetic analysis of > indefinite division in human cells: Evidence > for a cell-senescence-related gene(s) on > human chromosome 4. PNAS 88:5635-5639. 52 > > Ryan, P.A. et al (1994) Failure of Infinite Life > span human cells from different immortality > complementation groups to yield finite life > span hybrids. J. Cell. Phys. (in press) > >2. vs. DNA damage: >[The fact that senescence is a dominant property >suggests that DNA damage is not responsible for >the senescence phenomenon. If senescent cells had >lost a function that immortal cells retained, >then immortality would be dominant. >It seems unlikely that senescence would be due >to a gain of function mutation in all senescent >cells simultaneously. If immortality were due >primarily to a gain of function mutation not present in >senescent cells, again immortality would be >expected to dominate. The remaining possibility >then is that immortality is due to a loss of function, >and that senescent cells have retained the normal >genotype.] 6 >3. telomere shortening: >It was originally observed by Crick around >1960 (I think) that the DNA replication machinery, >which can only synthesize in one direction, would > always leave a little bit of unreplicated DNA >on the lagging strand at the telomere (end of the >chromosome). Proteins were identified which could >extend telomeres, which have a special sequence. >It is now well established that human telomeres >get shorter on average as a function of age, that >they are elongated in sperm cells, that as >cells senesce in culture their telomeres shorten with >a striking uniformity. It has been proposed that >telomere shortening is responsible for cell >ce and hence is involved in the aging >process, but no causal role has emerged. >Evidence against the telomere hypothesis: Telomere >shortening in yeast leads to cell death, not >the phenotype seen in mammalian cell senescence;9 > >Mouse telomeres are up to ten times as long as > human telomeres and do not shorten over the >lifetime, and yet mouse cells senesce faster >that human cells in culture. > >References: > Kipling, D. & Cooke, H.J. (1990) Hypervariable > ultra-long telomeres in mice. Nature 347:400-402. > Lundblad, V. & Szostak, J. W. (1989) A Mutant > with a Defect in Telomere Elongation Leads to > Senescence in Yeast. Cell 57:633-643. > Allsopp, R.C. et al. (1992) Telomere Length > predicts replicativcapacity of human > fibroblasts. PNAS 89(21):10114-8. > >3. senescence of the immune system: > >F. Cellular Aging > >G. Oxidative Stress Hypothesis64 > >With the random damage model falling out of favor, the >free radical theory has evolved into what is termed >the "oxidative stress hypothesis", which asserts that >modification and damage to cellular molecules by free >radicals is capable of altering "genetic programs" and >disrupting cell function, thereby contributing to aging >regardless of DNA damage. This model draws >support from observations that (1) the free hydroxyl >radical can clearly contribute to biochemical pathways >producing not only damaged DNA but >dysfunctional and/or deleterious >proteins and lipids; (2) levels of such "oxidative stress" >have been illustrated to increase throughout the lifespans >of humans and drosophila [ and c. elegans? ], and is >consistent with the results of rodent dietary restriction; >(3) there is a clear correlation >between lifespan and oxygen consumption/body weight > weight in a number of species; (4) recent work in >drosophila has extended lifespan by manipulating the > biochemical pathway which metabolizes superoxide and hydrogen7 > >peroxide. There is extensive literature on oxidative stress. >The genes/proteins involved in free radical metabolism are >well-known (see SOD, catalase, glutathione peroxidase >in any biochemistry textbook) but their regulation is not >well understood. [Enzymes are regulated by their >substrate and product levels, a "gimme"] >Downstream events (i.e., exactly which >important proteins and lipids are modified/damaged) is also >not clear. >References: > Sohal, R.S. & Allen, R.G. (1990) Oxidative Stress as a > causal factor in differentiation and aging: a > unifying hypothesis. Exp. Gerontology 25:499-522. > Stadtman, Earl R. (1992) Protein Oxidation and Aging. > Science 257:1220-1224. > > >H. DNA methylation > >Methylation of cytidine residues of DNA has been correlated 70 > >with gene expression levels in a number of cases. >It is unresolved whether methylation is a cause or >result of altered chromatin structure. DNA methylation >is thought to be responsible for imprinting, and >has been implicated as a mechanism in both >development and aging. Overall methylation >levels in mice apparently decrease >as a function of age from six to twenty-four >months, and may subsequently increase. >There is an extensive literature on DNA methylation >and aging studies are only a small part of >this active field. >References: > Singhal, R.P. (1987) DNA methylation in Aging of Mice. > Mechanisms of Ageing and Development, 41:199-210. > > >j. Other > >III. Aging in model organisms 3 > > >Traditional approaches to genetic and biochemical study >include making mutants, and fractionating >extracts and assaying for activity. Generating >mutant humans and dissecting them is clearly not >as ethical, so traditional laboratory organisms are >used in many aging studies. This has an advantage >that experiments can be performed ethically and >efficiently, but a >disadvantage that the results may not apply to humans. >Aside from obvious morpohological differences, perhaps >the strongest argument is that since humans live so long, >our genome must have overcome whatever it is that >causes other organisms to have such short lifespans. On the >other hand, aging even in fruit flies and worms has a >striking resemblance to that in humans. > >A. Humans >1. biomarkers of aging in humans: >7 > >2. causes of death: I am having a hard time finding > a simple summary of U.S. mortality statistics > and would appreciate anyone's contribution > here. What I have found is that approximately > 40% of all persons will have a neoplasm in > heir lifetime and that for about 20% of the > population this is the cause of death. George > Will discussed Sherwin B. Nuland's latest book > "How We Die: Reflections on Life's Final Chapter" > in the March 7 1994 Newsweek, and claimed that > 85% of the aging population "succumbs[s] to > one of seven ailments - atherosclerosis, > hypertension, adult-onset diabetes, obesity, > Alzheimer's and other dementias, cancer, > and decreased resistance to infections". The > book is apparently quite morbid in its >attention to detail, and I suppose I will try > to find it although I'm frankly not looking > forward to reading the thing.82 > >3. progeroid syndromes: A number of hereditary disorders >result in short lifespans during which the >senescence process is apparently accelerated. >None of them exactly matches the wild-type >aging phenotype, but the similarities are >quite striking, and one would expect genes causing >these syndromes to be significant in regulating the >aging process. Traditional genetic linkage >analyses are difficult because the diseases are >very rare autosomal recessive. A linkage for >Werner's syndrome was announced two years ago >but I haven't heard of a gene yet. A number of >progeroid syndromes have been linked to >DNA repair deficiencies, and Werner's has > reported mutator phenotype. [The distinction >etween DNA repair and general transcription >nd replication is not entirely clear at this >point. It is interesting that not all cellular >mutator phenotypes result in premature aging >syndromes in the organism.]6 > > References: > Goto, M. et. al. (1992) Genetic Linkage of Werner's > syndrome to five markers on chromosome 8 > Nature, 355:735-737 (20 Feb '92) > > >4. linkages to longevity: A recent publication reports >the distribution of alleles implicated in >cardiovascular risk at two loci (genes) between >French centenarians and >a control population aged 20-70. The study was >quite large and different distributions were found >at both loci. The paper refers to an established >linkage between longevity and HLA genotype >s well. [Also I believe it is common knowledge >that women live generally longer than men, making >the Y chromosome a significant longevity determinant.] >References: > Schachter, F. et. al. (1994) Genetic associations > with human longevity at the APOE and ACE loci.9 > > Nature Genetics 6:29-32 (january 1994). > >5. hormone studies: >B. Rodents - mice are the most common mammalian experimental >model for genetic research. The mouse is >considered to to fairly closely model humans. >Murine cells are easily transformed in culture. >Mice may have fewer defenses against dysplasia >because they are smaller and don't live as long. > >1. calorie restriction: It was first observed in the >1930's that rats which were fed less but suppli >with proper nutrition lived longer. It has since >been determined that the caloric intake is the >sole determinant, suggesting that metabolic rate >metabolic rate serves as a "genetic clock". However, >metabolic rate is not necessarily lowered when the >reduced mass of the animal is corrected for. The >fact that a large number of physiological and 93 > >pathological symptoms of aging are delayed in CR >animals has made the phenomenon difficult to > study. As glucose, insulin, and plasma-free >glucocorticoid concentrations are affected, > modulation of neuroendocrine regulatory > systems has been implicated. The onset of tumors, > which kill about 50% of all mice, is delayed in > CR mice. No direct evidence > exists for any hypothesis regarding the > effects of CR. >References: > Masoro, E.J. (1993) Dietary Restriction and Aging. > J. of the Am. Ger. Soc. 41:994-999. > Weindruch, R. (1989) Dietary Restriction, Tumors, > and Aging in Rodents. J. of Geron. 44(6):67-71. > >2. SAM (senescence accelerated mouse): >3. SOD transgenics > >C. Drosophila 6 > >1. Genetic analysis > >2. engineered mutants: Flies with extra copies of >both Superoxide Dismutase, which converts >superoxide anion radical to H2O2, and Catalase, >which converts H2O2 to water and oxygen, were shown >to have moderately increased lifespan and >slightly delayed loss of physical activity. >Cellular oxidative stress was clearly reduced >as measured by protein carbonyl content. > >References: Orr, W.C. & Sohal, R.S. (1994) > Extension of Life-Span by Overexpression of > Superoxide Dismutase and Catalase in Drosophila > melanogaster. Science 263:1128-1130 (25 Feb '94) > >D. C. Elegans >1. backcross analysis >2. age-1 mutant > 2. "Methuselah": A recently reported mutant now holds9 > > the record for increase in lifespan. A mutation >in daf-2, a developmental gene, more than doubles > nematode lifespan (18 to 42 days mean). The mutants >are "healthy and fertile". >References: > Kenyon, C. et al. (1993) A C. elegans mutant that lives > twice as long as wild type. Nature 366:461-464. > See also News & Views (Pertridge & Harvey) > from the same issue. > > >E. Other Species > >1. yeast >2. sea urchin >3. calorie restriction in primates >F. Relationship of biomarkers of aging in humans to >those in model organisms > >IV. Other interesting phenomena, etc. 100% Reposted by Jan (John) Coetzee Rate This Message: http://www.cryonet.org/cgi-bin/rate.cgi?msg=3277